Surgical treatment of Lutembacher syndrome
Araki, J.; Koizumi, S.; Abe, Y.; Kahata, O.; Yokoyama, A.; Sato, S.; Sato, K.; Tabayashi, K.; Onodera, H.; Kagawa, Y.; Mohri, H.; Horiuchi, T.
Nihon Kyobu Geka Gakkai 28(9): 1398-1402
1980
ISSN/ISBN: 0369-4739 PMID: 7430721 Document Number: 164769
Patients (13) with Lutembacher syndrome, defined as secundum atrial septal defect associated with mitral stenosis or regurgitation, underwent surgical treatment. Three patients with mitral stenosis were aged 28-38 yr and were in New York Heart Association Functional Class II, III and IV, respectively. Open mitral commissurotomy and suture closure of atrial septal defect were performed in all patients with good results. Ten patients associated with mitral regurgitation were aged 2-51 yr. Their clinical severity was closely related to the degree of mitral regurgitation: 4 of 10 who were in functional Class IV had extreme regurgitation over grade 3 of Sellers' classification. Atrial septal defect was repaired by suture closure in 4, with dacron patch in 6. Mitral regurgitation was treated by valve replacement with Bjork-Shiley prosthesis or porcine xenograft in 4, valvuloplasty in 2 and annuloplasty in 2. Mitral valve was not repaired in 2 patients with minimal regurgitation. Excellent operative results were obtained in all except 1 operative death. Lesions of the mitral varied such as annular dilatation, cleft of the anterior leaflet, prolapsing leaflet, torn chordae, subacute bacterial endocarditis and rheumatic valvulitis.