Congenital cystic dilatation of the intrahepatic bile ducts. Caroli's disease and its complications
Seefeld, U.; Jaeger, M.; Akovbiantz, A.; Maranta, M.; Heinzel, F.; Schmid, M.
Schweizerische Medizinische Wochenschrift 109(20): 758-762
1979
ISSN/ISBN: 0036-7672 PMID: 451501 Document Number: 154051
Two cases with congenital dilatations of the intrahepatic bile ducts are reported. The clinical, diagnostic and therapeutic aspects and possible complications of this rare disease are discussed. The well-known frequent occurrence of cholangiocarcinoma in Caroli's disease is illustrated by one of our patients. Because of the limited therapeutic possibilities, the prognosis of this illness remains unfavourable.