Baker-Winegrad disease (hepatomegaly, hypoglycemia during fasting, hyperlactacidemic metabolic acidosis, hepatic fructose-1-6-diphosphatase deficiency) . Presentation of the 1st Italian case and pathogenetic hypothesis
De Prà, M.; Laudanna, E.
Minerva Pediatrica 30(24): 1973-1986
1978
ISSN/ISBN: 0026-4946 PMID: 224299 Document Number: 134670
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