Heredo-ataxia and cochleo-vestibular disorders
Van de Heyning, P.H.
Acta Oto-Rhino-Laryngologica Belgica 32(6): 671-684
1978
ISSN/ISBN: 0001-6497 PMID: 377906 Document Number: 127019
Cochleo-vestibular dysfunction of patients suffering from a heredo-ataxia, have been frequently described. A family and a single case are presented, which show the association of a heredo-ataxia, more specifically the Roussy-Lévy syndrome, progressive sensorineural loss, nystagmus and vestibular a- or hyporeflexia. A review of the literature is included and the standpoints concerning the nosological entities are discussed.